Peripheral nerve sheath tumors, also called neurofibrosarcomas, are malignant tumors that form in the soft tissues surrounding the peripheral nerves, which receive messages from the brain and stimulate voluntary movement. These tumors are usually found in the arms and legs and can spread extensively along nerve tissue.
Patients with peripheral nerve sheath tumors are treated at Dana-Farber/Boston Children's Cancer and Blood Disorders Center through the Bone & Soft Tissue Program. Continue reading to learn more about peripheral nerve sheath tumors or visit the Bone & Soft Tissue Program homepage to learn about our expertise.
Children with neurofibromatosis type 1 are at very high risk of developing these tumors. Because they affect tissue that is elastic and easily moved, peripheral nerve sheath tumors may exist for a long time before they are diagnosed. The most common symptoms include:
In addition to a complete physical exam, a doctor may order the following to diagnose a peripheral nerve sheath tumor:
After all tests are completed, doctors will be able to outline the best treatment options.
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